Retroperitoneal Cystic Lymphangioma : case report: Case Report

Khalid JAMALEDDINE; Amal HAJRI; Rida LAABOULI; Anas ELWASSI; Driss ERGUIBI; Rachid BOUFETTAL; Saad RIFKI JAI; Farid CHEHAB

doi:10.58372/2835-6276.1111

Authors

Khalid JAMALEDDINE Department of general surgery, Ibn ROCHD University hospital of Casablanca, Casablanca
Amal HAJRI Department of general surgery, IBN ROCHD University hospital of Casablanca, Casablanca, Morocco
Rida LAABOULI Department of general surgery, IBN ROCHD University hospital of Casablanca, Casablanca, Morocco
Anas ELWASSI Department of general surgery, IBN ROCHD University hospital of Casablanca, Casablanca, Morocco
Driss ERGUIBI Department of general surgery, IBN ROCHD University hospital of Casablanca, Casablanca, Morocco
Rachid BOUFETTAL Department of general surgery, IBN ROCHD University hospital of Casablanca, Casablanca, Morocco
Saad RIFKI JAI Department of general surgery, IBN ROCHD University hospital of Casablanca, Casablanca, Morocco
Farid CHEHAB Department of general surgery, IBN ROCHD University hospital of Casablanca, Casablanca, Morocco

DOI:

https://doi.org/10.58372/2835-6276.1111

Keywords:

Lymphangioma, retroperitoneal cyst, surgical cyst resection

Abstract

Lymphangiomas, cystic hygroma or macrocystic lymphatic malformation are a rare and benign congential malformations of the lymphatic system. Adults are affected rarely and less than children, and the abdominal location even less.

Here, we discuss the case of a 56years old woman admitted and operated for a 7cm cystic mass of the tail of the pancreas, whom per operative exploration showed a retroperitoneal polycystic mass and histopathology concluded a lymphangioma.

Less than 1% affect the retroperitoneum, they typically occur in spaces surrounded by loose connective tissue, the are difficult to differentiate from a mucinous cystic neoplasm of the pancreas by imaging since both have the appearance of multilocular cysts. Ultrasonography is very sensitive and relatively specific for evaluation of abdominal cystic masses. Laparoscopic removal has certain advantages over classical laparotomy, complete excision is recommended to protect the patient from subsequent recurrences even though cystic lymphangiomas are low-grade malignancies.

The diagnosis of CL often is facilitated by means of modern imaging. Differential diagnosis include pancreatic pseudocysts, mucinous and serous cystadenomas, other congenital cysts and pancreatic ductal carcinoma with cystic degeneration. If symptomatic lesions or complications arise, complete surgical excision is a must.

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